Case Report

Pulmonary congenital cystic adenomatoid malformation: a rare congenital abnormality in adults and review of literature

Iftikhar Ahmed Chaudhry*, Mohammad Nasim Khan, Yousif A Alqahtani, Abdullah Alghamdi, Othman M AlFraih, Meenal A AlAbdulhai and Ikram Ul-Haq Chaudhry

Published: 25 November, 2022 | Volume 6 - Issue 2 | Pages: 016-019

Congenital cystic adenomatoid malformation of the lung (CCAM) is characterized by an adenomatoid proliferation of bronchiole-like structures and cysts formation. The condition is most commonly found in newborns and children and may be associated with other malformations; rarely, the presentation is delayed until adulthood. We herein report two cases of CCAM in adult patients. 22 years old healthy female with pre-employment health screening chest x-Ray showed a lesion in the upper lobe of the right lung. In another case, a computed tomographic scan of the thorax (CT) confirmed a mass in the upper right lung. A 28-year-old male presented with recurrent respiratory tract infection resistant to antimicrobial therapy. CT scan of the thorax showed a mass in the left lung upper zone. Surgical resection was performed in both cases, and histopathology of the resected specimen showed both cases were consistent with the CCAM.

Read Full Article HTML DOI: 10.29328/journal.jprr.1001038 Cite this Article Read Full Article PDF


Congenital cystic adenomatoid; Malformation; Malignancy; Respiratory tract infection; Surgery


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